La nephroblastomatose: a propos de deux cas

ABSTRACT

Rare entity recently individualized, Nephroblastomatosis refers to the finding of accumulations of metanephric blastema in infants and children at any time beyond 36 weeks gestation or in an abnormal location or quantity in younger infants. Two subtypes -Multifocal superficial Nephroblastomatosis; -Diffuse Nephroblastomatosis Malformations associated could lead to emphasize the hypothesis of genetical abnormality. It may be confused with bilateral Nephroblastoma. Our purpose will be to describe the clinical, radiological, pathological features and the prognosis of Nephroblastomatis in one hand, and in the other hand the close embryogenic and encogenic relationship between Nephroblastoma and Nephroblastomatosia