Mammary analogue secretory carcinoma of parotid gland in a teenage boy

ABSTRACT

Mammary analogue secretory carcinoma [MASC] is a rare salivary gland malignancy that exhibits resemblance with secretory carcinoma of the breast [SC] due to the presence of ETV6-NTRK3 gene fusion, formerly classified as acinic cell carcinoma. It is a slowly growing painless tumor that exhibits wide range of clinical behavior. This tumor typically affects middle aged people. Less than 100 such cases have been reported in the literature so far with only 8 case reports of patients less than 19 years of age. Very little is known about the clinical management of such cases. We hereby report a case of 15-year boy who had been managed for MASC of left parotid gland with exision