Angioimmunoblastic lymphadenopathy with dysproteinemia complicated by pancytopenia

ABSTRACT

Angioimmunoblastic lymphadenopathy with dysproteinemia [AILD] is described. The patient had generalised lymphadenopathy, skin rash and hepatosplenomegaly. Serum IgA level was raised. Lymphnode biopsy showed effacement of its architecture, infiltration by numerous immunoblast and plasma cells and abundant proliferation of arborising small blood vessels. After initial improvement on steroid, the patients 's general condition deteriorated and he developed pancytopenia and died