E.N.T. abnormalities in arthrogryposis multiplex congenita

ABSTRACT

Arthrogryposis multiplex congenita is a congenital failure of the development of the skeletal muscles. It may be neuropathic or myopathic. Affection of the hard palate may be severe enough, especially in the myopathic type to cause otorhinolaryngology abnormalities. This may lead to disorders of speech or malfunction of the Eustachian tubes, with its sequelae, that might present to the otorhinolaryngologist and necessitate its management and follow up