fibrose pulmonaire idiopathique [A' propos d'un cas]

ABSTRACT

The idiopathic pulmonary fibrosis is a rare affection in pediatrics pathology. It is a chronic disease that has evolved throughout a small period to reach death due to the respiratory inflammation. Hamman and Rich as a diagnostic of exclusion which makes the diagnostic difficult. The diagnostic of IPF is confirmed only by histologic evaluation, since it is mainly dependent on the interrogative, a clinical test and paraclinical arguments. The diagnostic which last a long period is harmful since the average of survival is less than 5 years. The medical treatment depends on the prescription of corticoids and eventually over those immunosuppressors. This treatment is relatively less efficient rapid, in this way a pulmonary transplantation should be considered. This Work was incited by a case of IPF, diagnosed after child's death. This child has benefited with a large therapy. Nonetheless, he died by respiratory insufficiency. In order to understand this affection disease, we have created a literary magazine of the IPF so that a precocious and an adequate knowledge of this mortal affection would be taken into consideration and acknowledged