Long term follow-up of surgrically treated skeletal deformities in osteogenesis imperfecta

ABSTRACT

In this study we evaluate the long term functional results in surgically treated Osteogenesis Imperfecta [O.I.] patients. The goals of our treatment are to maximize function, minimize deformity and disability. We reviewed 128 patients with O.I. who presented to the out patients Orthopaedic Department of the Paediatric Hospital, Cairo University. In this study we present the functional results in 31 surgically treated patients who responded to our letters among 62 operated children scince 1984. Most of the children were operated upon at a delayed age [average 6.5 years]. Our follow-up period range from 4 to 14 years [average 7 years]. None of these patients attended their follow-up dates on a regular basis, and our policy was to review them every 6 months. Revision surgeries were done for a large mumber of patients [71%]. Complications following surgery were common. At the final examination, there were only 4 patients walking without aid