Adamantinoma of tibia: a case report

ABSTRACT

Adamantinoma is a rare primary malignant tumor of the long bones with unknown pathogenesis. So far only a few cases are reported in the literature [2,3,9,11,17]. Tibia is the major site of predilection, however, the tumor also reported occasionally in other long bones such as femur, fibula, humerus, ulna and radius [1,8,12]. Most of the patients are in the second and third decades of life. Rarely fibrous dysplasia [5] is associated with adamantinoma of the long bones. The symptoms are long standing. The routine radiologic finding is that of multiple lucent zones interspersed with sclerotic bone,usually with one large rarefied area in the mid shaft.Histologically, islands of epithelial cells with peripheral palisading are seen in fibrous stroma. Histogenesis of this tumor is not yet clear. But majority of the believe that of epithelial origin [6,15,16,18].Treatment depends upon the extent of tumor. If it is surgic feasible, resection of the tumor is the treatment choicet if not, amputation. Here we report one case of adamantinoma of tibia and discuss clinicopathological findings: