Porokeratosis of Mibelli: an uncommon genodermatosis

ABSTRACT

Porokeratosis of Mibelli is an uncommon, inherited, autosomal dominant disorder characterized by disordered epidermal keratinization and by a predisposition to develop malignant transformation. A case of this rare disorder with classical presentation in a teen aged boy is reported here, which was managed with topical retinoid, superficial chemical peeling and sunscreen lotion