Supravalvular mitral Ring - A rare type of congenital mitral Stenosis - two case reports

ABSTRACT

Supravalvular mitral ring [SVR] is a very rare type of congenital mitral stenosis [MS]. It is in the form of a Supravalvular circumferential ridge arising at the base of the atrial aspect of the mitral leaflets. We report here two cases of SVR. One case is isolated SVR and the other case is SVR with associated ostiumprimum atrial septal defect [ASD] which is a common associated anomaly with SVR. Careful echocardiography should be done in order not to miss this very rare type of congenital MS