Malignant paraganglioma of the organ of Zukerkandl

ABSTRACT

The authors report the case of a patient operated on 1999 because of a paraganglioma of the Zukerkandl's organ. The diagnosis of the paraganglioma has been based on the analysis of the resected piece. Thirty-one months later, she developed medullar compression. The diagnosis of the malignant paraganglioma is confirmed in front of the presence on cromaffin tissue at the level of the affected vertebra. This case illustrates the diagnostic difficulty of this type of tumour before surgery as well as to establish immediate prognosis of this affection. The authors emphasise in this occasion the necessity of a prolonged supervision in order to screen the superview of recurrence or metastases in this localisation known to be malignant in more than the half of the cases