[Pulmonary alveolar proteinosis in two siblings. A case report]
Tunisie Medicale [La]. 2005; 83 (8): 488-491
in French
| IMEMR
| ID: emr-75401
ABSTRACT
Pulmonary alveolar proteinosis [PAP] is a rare disorder in children. This report describes two siblings in whom PAP developed during infancy [three years for the boy and four years two months for the girl]. The girl was admitted for chronic respiratory distress. Chest x-ray showed a reticulonodular pattern. Her brother was asymptomatic. The diagnosis of PAP was confirmed by open lung biopsy for the boy and broncho-alveolar lavage for the girl. Therapeutic broncho-alveolar lavages were performed [six for the girl and two for the boy], the girl lost dependence on oxygen therapy. 6 years later, the brother is still asymptomatic. The sister had two episodes of respiratory distress, after two and four years, that required therapeutic lavages. The last therapeutic broncho-alveolar lavage was performed for the first time by a Tunisian team
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Index:
IMEMR (Eastern Mediterranean)
Main subject:
Respiratory Insufficiency
/
Child, Preschool
/
Bronchoalveolar Lavage
Type of study:
Case report
Limits:
Female
/
Humans
/
Male
Language:
French
Journal:
Tunisie Med.
Year:
2005
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