Sinus histiocytosis with massive lymphadenopathy [Rosai-Dorfmans Disease] as cause of isolated hilar lymphadenopathy and complete remission after high dose steroid
Saudi Medical Journal. 2008; 29 (5): 763-765
in English
| IMEMR
| ID: emr-90189
ABSTRACT
Rosai-Dorfman's Disease, also known as sinus histiocytosis with massive lymphadenopathy SHML, is a rare histiocytic proliferative disorder and a distinct clinico-pathological feature of unknown origin. Painless cervical lymphadenopathy is the most common clinical presentation. Different treatment modalities have been tried with variable responses, however, there is no consensus on the best modality of treatment. Here, we present a case report of SHML causing isolated hilar lymphadenopathy with complete remission for more than 6 years, after a short course of high dose steroid dexamethasone 20 mg daily for 3 days
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Index:
IMEMR (Eastern Mediterranean)
Main subject:
Steroids
/
Thorax
/
Dexamethasone
/
Radiography, Thoracic
/
Tomography, X-Ray Computed
/
Lymphatic Diseases
Type of study:
Case report
Limits:
Humans
/
Male
Language:
English
Journal:
Saudi Med. J.
Year:
2008
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