Single stage repair and reconstruction of trigonocephaly and fronto orbito ethmoidal encephalocele

ABSTRACT

A nine- year-old Iranian girl presented with trigonocephaly and frontonasal deformity secondary to encephalocele of fronto orbito ethmoidal region. She had undergone an attempt to correct the deformity at the age of three. The case was managed by a single stage repair and reconstruction of both fronto orbito nasal deformity and trigonocephaly along with plication of the herniating encephalocele. Fronto nasal deformity, interorbital hypertelorism nasal deformity and associated trigonocephaly are the main aesthetic concerns in the management of craniofacial disfigurement associated with fronto ethmoidal encephalaceles. A single stage repair and reconstruction of these cases is always preferred