Clear cell sarcoma of kidney in an adult: a rare unsuspected entity

ABSTRACT

Clear cell sarcoma of the kidney is a highly malignant pediatric renal neoplasm occurring most frequently in the second to third year of life. Its occurrence in adults is extremely rare and a subject of isolate case reports. This neoplasm must be differentiated from other sarcomatoid tumors, sarcomas and round cell tumors because of its unique histomorphologic characteristics and mode of treatment. We present a rare case of Clear cell sarcoma of the kidney, presenting in adulthood with emphasis on its differential diagnosis