Nevoid basal-cell syndrome: literature review and case report in a family
São Paulo med. j
;
113(3): 917-21, May-Jun. 1995. ilus, tab
Article
in English
| LILACS
| ID: lil-161543
RESUMO
The Nevoid Basal-Cell Carcinoma Syndrome (NBCC), or as it is also referred to, basal-cell nevus syndrome or Gorlin-Goltz syndrome, is characterized by multiple early-appearing basal cell carcinomas, keratocytosis of the mandible, and anomalies of the ocular, skeletal reproductive system. We describe four patients in the same family, all of them possessing a large number of skin tumors associated with other typical clinical and X-Ray anomalies of NBCC. The definitive treatment of NBCC has yet to be established, however, early diagnosis is very important as well as the periodical follow-up examination of ten patients, mainly due to the transformations in the skin lesions that may occur.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Skin Neoplasms
/
Basal Cell Nevus Syndrome
Type of study:
Diagnostic study
/
Screening study
Limits:
Adult
/
Female
/
Humans
/
Male
Language:
English
Journal:
São Paulo med. j
Journal subject:
Cirurgia Geral
/
Cincia
/
Ginecologia
/
Medicine
/
Medicina Interna
/
Obstetr¡cia
/
Pediatria
/
Sa£de Mental
/
Sa£de P£blica
Year:
1995
Type:
Article
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