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Cardiomiopatia hipertrófica apical acometendo o ventrículo direito / Apical Hypertrophic Cardiomyopathy with Right Ventricular Involvement
Albanesi Filho, Francisco Manes; Castier, Marcia Bueno; Diamant, José David Aron; Lopes, Justiniano Simões; Lopes, Alberto Siqueira; Ginefra, Paulo.
  • Albanesi Filho, Francisco Manes; Universidade do Estado do Rio de Janeiro (UERJ). Hospital Universitário Pedro Ernesto. Rio de Janeiro. BR
  • Castier, Marcia Bueno; Universidade do Estado do Rio de Janeiro (UERJ). Hospital Universitário Pedro Ernesto. Rio de Janeiro. BR
  • Diamant, José David Aron; Universidade do Estado do Rio de Janeiro (UERJ). Hospital Universitário Pedro Ernesto. Rio de Janeiro. BR
  • Lopes, Justiniano Simões; Universidade do Estado do Rio de Janeiro (UERJ). Hospital Universitário Pedro Ernesto. Rio de Janeiro. BR
  • Lopes, Alberto Siqueira; Universidade do Estado do Rio de Janeiro (UERJ). Hospital Universitário Pedro Ernesto. Rio de Janeiro. BR
  • Ginefra, Paulo; Universidade do Estado do Rio de Janeiro (UERJ). Hospital Universitário Pedro Ernesto. Rio de Janeiro. BR
Arq. bras. cardiol ; 68(2): 119-124, Fev. 1997.
Article in Portuguese | LILACS | ID: lil-320365
ABSTRACT
We report right ventricular involvement in apical hypertrophic cardiomyopathy (HCMP) in two women and one man, aged from 19 to 44 years-old, who presented different signs from those with left ventricular disease (who have good clinical evolution), with signs and symptoms of severe diastolic restriction, showing great atrial enlargement and two with atrial fibrillation and death due to thromboembolism. The right ventricular involvement in apical HCMP leads to a worst prognosis than isolated left ventricular disease, does not have the typical electrocardiographic changes and presents with ventricular restriction and tricuspid regurgitation.
Subject(s)
Full text: Available Index: LILACS (Americas) Main subject: Cardiomyopathy, Hypertrophic / Ventricular Dysfunction, Right Type of study: Etiology study / Observational study / Prognostic study Limits: Adult / Female / Humans / Male Language: Portuguese Journal: Arq. bras. cardiol Journal subject: Cardiology Year: 1997 Type: Article Affiliation country: Brazil Institution/Affiliation country: Universidade do Estado do Rio de Janeiro (UERJ)/BR

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Full text: Available Index: LILACS (Americas) Main subject: Cardiomyopathy, Hypertrophic / Ventricular Dysfunction, Right Type of study: Etiology study / Observational study / Prognostic study Limits: Adult / Female / Humans / Male Language: Portuguese Journal: Arq. bras. cardiol Journal subject: Cardiology Year: 1997 Type: Article Affiliation country: Brazil Institution/Affiliation country: Universidade do Estado do Rio de Janeiro (UERJ)/BR