Systemic congenital lymphangiomatosis
São Paulo med. j
;
114(5): 1278-1281, Sep.-Oct. 1996.
Article
in English
| LILACS
| ID: lil-320851
ABSTRACT
Systemic lymphangiomatosis is a rare disease characterized by the exageration of lymphatic channel proliferation, occurring in children and young adults. We describe an extremely rare case of congenital systemic lymphangiomatosis in a newborn who had ascitis and respiratory failure develop immediately after delivery. Death occurred during the first hour of life. Autopsy findings showed numerous cysts in soft tissues of the cervical area, mediastinum and diaphragm, and several other organs including the liver, spleen, thyroid and kidneys. The severe and diffuse involvement with cysts in both lungs by lymphangiomatosis was associated with poor prognosis and death in our case.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Lymphangioleiomyomatosis
Type of study:
Prognostic study
Limits:
Female
/
Humans
/
Infant, Newborn
Language:
English
Journal:
São Paulo med. j
Journal subject:
Cirurgia Geral
/
Cincia
/
Ginecologia
/
Medicine
/
Medicina Interna
/
Obstetr¡cia
/
Pediatria
/
Sa£de Mental
/
Sa£de P£blica
Year:
1996
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Universidade Estadual Paulista (UNESP)/BR
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