Disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease
Arq. neuropsiquiatr
;
61(2A): 259-261, Jun. 2003.
Article
in English
| LILACS
| ID: lil-339497
ABSTRACT
OBJECTIVE:
The aim of this report is to describe a fatal disseminated thrombotic micoangiopathy with renal, pancreatic, and cerebral involvement in a patient with recently diagnosed adult's Still disease (ASD). CASE REPORT A previously healthy 15 year old girl was admitted to our hospital. According to the clinical and laboratory data the diagnosis of adult's still Disease was established. The treatment was begun and few days after an initial improvement a sudden neurologic deterioration with coma and seizures has occurred. Hours later the patient died. Clinical, laboratorial, and pathologic data will be presented.CONCLUSION:
To our knowledge this is the second description of a fatal disseminated cerebral thrombotic microangiopathy in a patient with adult's Still disease, but with a much more fulminating evolution than previously reported. Some etiopathogenic mechanisms could be shared in these two disorders explaining this coexistence
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Purpura, Thrombotic Thrombocytopenic
/
Still's Disease, Adult-Onset
/
Intracranial Thrombosis
/
Hemolytic-Uremic Syndrome
Limits:
Adolescent
/
Female
/
Humans
Language:
English
Journal:
Arq. neuropsiquiatr
Journal subject:
Neurology
/
Psychiatry
Year:
2003
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Santa Casa de Misericórdia de Vitória/BR
/
Universidade Federal do Espírito Santo/BR
Similar
MEDLINE
...
LILACS
LIS