Fibrohistiocitoma maligno em criança, após tumor de Wilms: relato de caso / Malignant fibrous histiocytoma after WilmsÆ tumor: a case report

RESUMO

Malignant fibrous histiocytoma is a rare tumor in children, and its responsible for 2 to 6 percent of pediatric sarcomas. The authors report the case of a child who developed soft tissue malignant fibrous histiocytoma, as well as several fibrous histiocytic skin lesions, following treatment for WilmsÆ tumor patients has been improving very much over the last years because of successful treatment with chemo- and radiotherapy. A small proportion of these cases present a risk of developing a second neoplasm; genetic traits may enhance this risk. The authors discuss in this study those fibrous histiocytic lesions and the use of electron microscopy for definitive diagnosis. The authors conclude that follow-up of these patients treated for WilmsÆ tumor is of great importance for early detection of another neoplasm.