Central pontine and extrapontine myelinolysis: report of a case with a tragic outcome
J. pediatr. (Rio J.)
; J. pediatr. (Rio J.);82(2): 157-160, Mar.-Apr. 2006. ilus, graf
Article
in En
| LILACS
| ID: lil-428497
Responsible library:
BR1.1
ABSTRACT
OBJECTIVE:
To report a pediatric case of central pontine and extrapontine myelinolysis, a rare neurological disease often associated with rapid correction of hyponatremia.DESCRIPTION A 15 year-old female adolescent developed locked-in syndrome during severe hyponatremia. Brain magnetic resonance imaging was consistent with the diagnosis of central pontine and extrapontine myelinolysis.COMMENTS:
Serum sodium correction should proceed slowly and cautiously, based upon a careful calculation of sodium deficit, in order to minimize metabolic stress and avoid the occurrence of this dreadful complication, which has a tragic outcome in most cases. There is no scientifically proved effective treatment for myelinolysis, and severe cases usually have a dismal prognosis.
Full text:
1
Index:
LILACS
Main subject:
Myelinolysis, Central Pontine
/
Hyponatremia
Type of study:
Etiology_studies
/
Prognostic_studies
Limits:
Adolescent
/
Female
/
Humans
Language:
En
Journal:
J. pediatr. (Rio J.)
Journal subject:
PEDIATRIA
Year:
2006
Type:
Article