Amiloidose pulmonar: relato de caso de achado radiológico da apresentação nodular em grande fumante / Pulmonary amyloidosis: radiographic finding of nodular opacities in a heavy smoker
J. bras. pneumol
;
33(3): 343-346, maio-jun. 2007. ilus
Article
in Portuguese
| LILACS
| ID: lil-461999
RESUMO
A amiloidose pulmonar é uma doença rara, caracterizada pelo depósito extracelular de proteínas fibrilares no pulmão. Amiloidose é um termo genérico para grupos heterogêneos de doenças, incluindo doença de Alzheimer e diabetes mellitus tipo II. Apresenta-se no aparelho respiratório sob as formas traqueobrônquica, nodular pulmonar e septal alveolar (parenquimatosa difusa). Relata-se o caso de uma mulher, tabagista (20 anos/maço), portadora de amiloidose nodular pulmonar, diagnosticada através de exames pré-operatórios à realização de colecistectomia videolaparoscópica.
ABSTRACT
Pulmonary amyloidosis is a rare disease, characterized by extracellular deposition of fibrillary protein in the lungs. Amyloidosis is a generic term for a heterogeneous group of diseases, including Alzheimer's disease and type 2 diabetes mellitus. In the respiratory system, it appears in various forms tracheobronchial; nodular pulmonary; and alveolar septal (diffuse parenchymal). We present the case of a woman who was a 20 pack-year smoker and had nodular pulmonary amyloidosis, as diagnosed through tests performed prior to laparoscopic cholecystectomy.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Lung Diseases, Interstitial
/
Amyloidosis
Type of study:
Diagnostic study
Limits:
Female
/
Humans
Language:
Portuguese
Journal:
J. bras. pneumol
Journal subject:
Pulmonary Disease (Specialty)
Year:
2007
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Hospital Monte Sinai/BR
/
SUPREMA/BR
/
Universidade Federal de Juiz de Fora/BR
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