Síndrome de Peutz-Jeghers: relato de caso / Peutz-Jeghers syndrome: case report
Rev. Col. Bras. Cir
;
35(3): 210-211, maio-jun. 2008. ilus
Article
in Portuguese
| LILACS
| ID: lil-487545
ABSTRACT
Peutz-Jeghers syndrome (PJS) is a dominant autosomal inherited disorder characterized by intestinal hamartomatous polyps in association with mucocutaneous melanocytic maculae. This syndrome is rare, and the frequency reaches from 1 in 60,000 to 1 in 300,000 people in the USA. The symptom presentations vary greatly in this disease. Some patients require minor clinical treatment while others undergo many hospitalizations and surgical treatments. In addition, patients with PJS have an increased risk for developing a variety of malignant tumors. The aim of the present study was to report one case studied of Peutz-Jeghers syndrome.
Full text:
Available
Index:
LILACS (Americas)
Language:
Portuguese
Journal:
Rev. Col. Bras. Cir
Journal subject:
General Surgery
Year:
2008
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Universidade Federal do Piauí/BR
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