Amiloidose traqueobrônquica primária / Primary tracheobronchial amyloidosis
J. bras. pneumol
;
34(10): 881-884, out. 2008. ilus
Article
in English, Portuguese
| LILACS
| ID: lil-496621
ABSTRACT
Tracheobronchial amyloidosis is an uncommon localized form of amyloidosis, characterized by amyloid deposits restricted to the trachea, main bronchi and segmental bronchi. We present the case of a retired 67-year-old man with long-term progressive dyspnea, wheezing and chest pain. A diagnosis of tracheobronchial amyloidosis was made after the third fiberoptic bronchoscopy and histological confirmation through Congo red staining of tissue samples.
RESUMO
A amiloidose traqueobrônquica é uma forma pouco comum de amiloidose localizada, caracterizada por depósitos amilóides limitados à traquéia, brônquios principais e brônquios segmentares. Nós apresentamos o caso de um homem aposentado de 67 anos com dispnéia progressiva de longa data, sibilância e dor torácica. O diagnóstico de amiloidose traqueobrônquica foi realizado após três fibrobroncoscopias e confirmação histopatológica com coloração vermelho congo.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Tracheal Diseases
/
Bronchial Diseases
/
Amyloidosis
Type of study:
Diagnostic study
/
Etiology study
Limits:
Humans
/
Male
Language:
English
/
Portuguese
Journal:
J. bras. pneumol
Journal subject:
Pulmonary Disease (Specialty)
Year:
2008
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Ministério da Educação/BR
/
Universidade Federal de Santa Maria/BR
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