Necrose digital em paciente com lúpus eritematoso sistêmico e esclerose sistêmica tratada com inibidores da fosfodiesterase / Digital necrosis treated with phosphodiesterase inhibitors in a patient with connective tissue disease
Rev. bras. reumatol
;
48(5): 306-308, set.-out. 2008.
Article
in Portuguese
| LILACS
| ID: lil-500206
RESUMO
Os inibidores da fosfodiesterase têm sido introduzidos, nos últimos anos, como novos agentes farmacológicos no tratamento dos pacientes com fenômeno de Raynaud e isquemia digital. Será descrito o caso de uma paciente com lúpus eritematoso sistêmico e esclerose sistêmica limitada apresentando fenômeno de Raynaud grave e necrose digital refratária à terapia. A paciente obteve excelente resposta à associação de imunossupressão e sildenafil.
ABSTRACT
The phosphodiesterase inhibitors have been used recently for the treatment of Raynaud's phenomenon and digital ischaemia. We report the case of a patient affected by systemic lupus erythematosus and limited systemic sclerosis who presented severe Raynaud's phenomenon with digital necrosis despite treatment. The patient presented an excellent response to the association of immunosuppressant therapy and sildenafil.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Phosphodiesterase Inhibitors
/
Raynaud Disease
/
Scleroderma, Systemic
/
Lupus Erythematosus, Systemic
/
Necrosis
Limits:
Female
/
Humans
Language:
Portuguese
Journal:
Rev. bras. reumatol
Journal subject:
Rheumatology
Year:
2008
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Universidade Federal de Ciências da Saúde de Porto Alegre/BR
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