Dermatofibrossarcoma protuberante / Dermatofibrosarcoma protuberans

RESUMO

Dermatofibrossarcoma protuberante é um tumor cutâneo raro, com baixo grau de malignidade, caracterizado pelo padrão de crescimento lento, infiltrativo e alta tendência de recorrência local após excisão cirúrgica. A alta taxa de recorrência deste tumor está correlacionada com uma conduta cirúrgica inadequada em decorrência das lesões serem confundidas comd dermatofibroma ou com quelóide. Este artigo de revisão analisa as características clínicas,etiopatogênicas e histológicas, bem como aspectos do tratamento e evolução do dermatofibrossarcoma.

ABSTRACT

Dermatofibrosarcoma protuberans is a rare cutaneous tumor of low malignant grade, characterized by a pattern of slow, infiltrative growth and a marked tendency to recur locally after surgical excision. The high rate of recurrence of this tumor is correlated with poor surgical management because lesions may be confused with dermatofibroma or keloid. This article reviews dermatofibrosarcoma with particular emphasis on the epidemiologic, clinical, and histological features of diagnosis, as well as treatment modalities and prognosis. This review confirms the importance of accurate diagnosis of primary lesion and the need for aggressive surgical treatment (excision of 3 cm of sur rounding tissue) to lower the incidence of localrelapse.