Anartria o apraxia del habla progresiva / Progressive anarthria or speech apraxia
Rev. chil. neuro-psiquiatr
;
46(2): 124-128, jun. 2008.
Article
in Spanish
| LILACS
| ID: lil-513807
ABSTRACT
Two cases of progressive anarthria are reported; we remark their close but distinct relation with speech apraxia. Both of them were older female, with a progressive loss of speech, bilateral paresis of lower face, tongue and palatal muscles. They also had mild pyramidal signs and a fronto-subcortical cognitive deterioration. Brain TC and MRI were within normal limits. One of them had a possible progressive supranuclear palsy, the other one a possible corticobasal degeneration. The analysis of similar cases reports let us to conclude than there are several pathologies that can cause a progressive pseudobulbar palsy. The final diagnosis must be by postmortem examination of the brain.
RESUMEN
Se presentan dos casos de anartria progresiva, discutiendo la relación o el diagnóstico diferencial con la apraxia del habla progresiva. En ambos casos se trataba de mujeres mayores de 65 años con un cuadro de pérdida progresiva del lenguaje oral, con diparesia facial, lingual y velar, deterioro cognitivo de tipo frontal y discretos signos piramidales. Las imágenes cerebrales estructurales fueron normales. Uno de ellos pudo corresponder a una parálisis supranuclear progresiva, la otra a una degeneración corticobasal. Se analiza la literatura, llegando a la conclusión de que existen una serie de cuadros que pueden presentarse con un síndrome pseudobulbar progresivo. El diagnóstico definitivo debiera ser patológico.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Apraxias
/
Dysarthria
Type of study:
Diagnostic study
/
Etiology study
Limits:
Aged
/
Female
/
Humans
Language:
Spanish
Journal:
Rev. chil. neuro-psiquiatr
Journal subject:
Neurology
/
Psychiatry
Year:
2008
Type:
Article
Affiliation country:
Chile
Institution/Affiliation country:
Universidad de Chile/CL
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