Caso para diagnóstico / Case for Diagnosis
An. bras. dermatol
;
84(6): 680-681, nov.-dez. 2009. ilus
Article
in English, Portuguese
| LILACS
| ID: lil-538460
RESUMO
Relata-se o caso de paciente do sexo feminino, de 9 anos de idade, com história de lesões bolhosas exclusivamente no dimídio direito, que acomete vários familiares de forma simétrica e cuja histologia evidencia acantólise tipo muro dilapidado, correspondendo, assim, a uma apresentação rara de mosaicismo na doença de Hailey-Hailey.
ABSTRACT
The case of a 9-year-old girl with a history of blistering lesions restricted to the right side of her body is described. Several family members are also affected in a symmetrical fashion. Histological examination showed acantholysis similar to a "dilapidated brick wall", corresponding to a rare presentation of mosaicism in Hailey-Hailey disease.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Pemphigus, Benign Familial
Type of study:
Diagnostic study
Limits:
Child
/
Female
/
Humans
Language:
English
/
Portuguese
Journal:
An. bras. dermatol
Journal subject:
Dermatology
Year:
2009
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Santa Casa de Belo Horizonte/BR
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