Elastose perfurante serpiginosa em portadora da síndrome de Down / Elastosis perforans serpiginosa in a patient with Down's syndrome
An. bras. dermatol
;
85(5): 691-694, set.-out. 2010. ilus, tab
Article
in Portuguese
| LILACS
| ID: lil-567832
RESUMO
A elastose perfurante serpiginosa é dermatose perfurante primária incomum, frequentemente associada a determinadas doenças genéticas e caracterizada por eliminação transepidérmica de fibras elásticas. Relata-se um caso raro dessa dermatose em paciente feminina de 19 anos, portadora da síndrome de Down, que apresentava pápulas eritematoceratóticas em arranjo arciforme, localizadas no antebraço e joelho direitos, assintomáticas, com cinco anos de evolução. Após confirmação histopatológica, foi iniciado tratamento com crioterapia, ocorrendo remissão parcial das lesões.
ABSTRACT
Elastosis perforans serpiginosa is a rare, primary perforating dermatosis, frequently associated with certain genetic diseases and characterized by the transepidermal extrusion of elastic fibers. The present case report describes this dermatosis in a 19-year old female patient with Down's syndrome, who presented with asymptomatic erythematous, keratotic papules in an arciform pattern, located on her right forearm and knee, which had been present for five years. Following histopathological confirmation, treatment with cryotherapy was initiated, resulting in partial remission of the lesions.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Skin Diseases
/
Down Syndrome
Limits:
Female
/
Humans
Language:
Portuguese
Journal:
An. bras. dermatol
Journal subject:
Dermatology
Year:
2010
Type:
Article
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