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Pentalogía de Cantrell. A propósito de un caso / Pentalogy of Cantrell. A case report
Hernández-González, Martha; Jiménez-Arteaga, Santiago; Ortega, Francisco; Solorio, Sergio; Martínez-Flores, Enrique; David-Gómez, Felipe; Sánchez-Soberanis, Agustín; Ortegón-Cerdeña, José; López-Gallegos, Diana; Argüero-Sánchez, Rubén; Alva, Carlos.
  • Hernández-González, Martha; Centro Médico Nacional Siglo XXI. Hospital de Cardiología. Servicio de Cardiopatías Congénitas. MX
  • Jiménez-Arteaga, Santiago; Centro Médico Nacional Siglo XXI. Hospital de Cardiología. Servicio de Cardiopatías Congénitas. MX
  • Ortega, Francisco; Centro Médico Nacional Siglo XXI. Hospital de Cardiología. Servicio de Cardiopatías Congénitas. MX
  • Solorio, Sergio; Centro Médico Nacional Siglo XXI. Hospital de Especialidades. Servicio de Hemodinamia. MX
  • Martínez-Flores, Enrique; Centro Médico Nacional Siglo XXI. Hospital de Cardiología. MX
  • David-Gómez, Felipe; Centro Médico Nacional Siglo XXI. Hospital de Cardiología. Servicio de Cardiopatías Congénitas. MX
  • Sánchez-Soberanis, Agustín; Centro Médico Nacional Siglo XXI. Hospital de Cardiología. Servicio de Cardiopatías Congénitas. MX
  • Ortegón-Cerdeña, José; Centro Médico Nacional Siglo XXI. Hospital de Cardiología. Servicio de Cardiopatías Congénitas. MX
  • López-Gallegos, Diana; Centro Médico Nacional Siglo XXI. Hospital de Cardiología. Servicio de Cardiopatías Congénitas. MX
  • Argüero-Sánchez, Rubén; Centro Médico Nacional Siglo XXI. Hospital de Cardiología. MX
  • Alva, Carlos; Centro Médico Nacional Siglo XXI. Hospital de Cardiología. Servicio de Cardiopatías Congénitas. MX
Arch. cardiol. Méx ; 76(2): 202-207, abr.-jun. 2006.
Article in Spanish | LILACS | ID: lil-569143
ABSTRACT
Ectopia cordis is an extremely rare cardiac anomaly. The heart is localized partially or totally outside the thorax cavity. This anomaly occurs as an isolated defect or combined with others midline defects. Cantrell and colleagues described, in 1958, a syndrome including defects of the abdominal wall, sternum, diaphragm, pericardium and heart. There are few successful surgical cases with this pentalogy. We describe a case with this Cantrell's pentalogy. The cardiac malformation was a univentricular heart with pulmonary stenosis. The patient underwent successful surgical palliation with a systemic-to-pulmonary anastomosis and uneventful recovering.
Subject(s)
Full text: Available Index: LILACS (Americas) Main subject: Pericardium / Sternum / Abnormalities, Multiple / Diaphragm / Abdominal Wall / Heart Defects, Congenital Limits: Child / Humans / Male Language: Spanish Journal: Arch. cardiol. Méx Journal subject: Cardiology Year: 2006 Type: Article Affiliation country: Mexico Institution/Affiliation country: Centro Médico Nacional Siglo XXI/MX

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Full text: Available Index: LILACS (Americas) Main subject: Pericardium / Sternum / Abnormalities, Multiple / Diaphragm / Abdominal Wall / Heart Defects, Congenital Limits: Child / Humans / Male Language: Spanish Journal: Arch. cardiol. Méx Journal subject: Cardiology Year: 2006 Type: Article Affiliation country: Mexico Institution/Affiliation country: Centro Médico Nacional Siglo XXI/MX