Budd-Chiari syndrome in association with Behçet's disease: review of the literature / Síndrome de Budd-Chiari em associação com a doença de Behçet: revisão de literatura
São Paulo med. j
;
129(2): 107-109, Mar. 2011. tab
Article
in English
| LILACS
| ID: lil-587836
ABSTRACT
The risk that patients with Behçet's disease may develop various thrombotic complications has been previously described. Although vascular complications from Budd-Chiari syndrome associated with Behçet's disease have been described, the pathogenic mechanisms are still unknown. Severe vascular complications present in Budd-Chiari syndrome associated with Behçet's disease are very common among young male adults. The objective of this study was to review the literature and present the association of Budd-Chiari syndrome with Behçet's disease.
RESUMO
O risco de pacientes com doença de Behçet desenvolverem várias complicações trombóticas já foi descrito. Apesar de complicações vasculares na síndrome de Budd-Chiari associada à doença de Behçet terem sido descritas, os mecanismos patogenéticos ainda são desconhecidos. Complicações vasculares graves presentes na síndrome de Budd-Chiari associada à doença de Behçet são muito mais comuns no adulto jovem do sexo masculino. O objetivo deste trabalho é o de revisar a literatura e apresentar a associação da síndrome de Budd-Chiari com a doença de Behçet.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Behcet Syndrome
/
Budd-Chiari Syndrome
Type of study:
Etiology study
/
Risk factors
Limits:
Humans
Language:
English
Journal:
São Paulo med. j
Journal subject:
Cirurgia Geral
/
Cincia
/
Ginecologia
/
Medicine
/
Medicina Interna
/
Obstetr¡cia
/
Pediatria
/
Sa£de Mental
/
Sa£de P£blica
Year:
2011
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Hospital Municipal de Campo Limpo/BR
/
Universidade de São Paulo/BR
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