Encefalomielitis aguda diseminada: [revisión] / Acute disseminated encephalomyelitis: [review]
Arch. venez. pueric. pediatr
;
71(4): 145-155, oct.-dic. 2008. ilus, tab
Article
in Spanish
| LILACS
| ID: lil-589234
RESUMEN
La encefalomielitis aguda diseminada (EMAD) es la leucoencefalopatía adquirida de mayor presentación en la edad pediátrica, de naturaleza inflamatoria-autoinmune, generalmente monofásica, polisintomática, y asociada a compromiso del estado de conciencia. Frecuentemente es precedida por un proceso infeccioso o por una inmunización. Se revisó la literatura médica de los últimos años considerando los aspectos etiopatogénicos, clínicos, diagnósticos y terapéuticos. Se presentan los últimos criterios diagnósticos para la EMAD y sus formas recurrentes, así como la importancia de los diagnósticos diferenciales, entre ellos la Esclerosis Múltiple Pediátrica(EMP). Las imágenes de Resonancia Magnética (IRM) constituyen el estudio de elección para detectar lesiones desmielinizantes.
ABSTRACT
Acute disseminated encephalomyelitis (ADEM) is an acquired leucoencephalopathy, that occurs more frequently during childhood, of inflammatory autoimmune condition, usually monophasic, polysymptomatic and associated with sensory deterioration. It is a frequently preceded by infections or vaccinations. Recent medical literature was reviewed considering etiology, pathogenesis, clinical, diagnosis and treatment aspects. The current diagnostic criteria for ADEM, its variants and the relevance of differential diagnostics, like Pediatric Multiple Sclerosis (PMS) are included. Magnetic Resonance Imaging (MRI) is recommended to detect demyelination injuries. High doses of steroids are still the therapeutic alternative for ADEM.
Acute disseminated encephalomyelitis; Autoinmune Desmielinización; Complejo Trimolecular; Encefalomielitis Aguda Diseminada; Esclerosis Múltiple Pediátrica; Esteroides; Resonancia Magnética; autoimmune; demyelination; diagnostics criteria; magnetic resonance imaging; pediatric multiple sclerosis; steroids; trimolecular complex
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Steroids
/
Magnetic Resonance Imaging
/
Encephalomyelitis, Acute Disseminated
/
Multiple Sclerosis
Type of study:
Etiology study
Limits:
Child
/
Female
/
Humans
/
Male
Language:
Spanish
Journal:
Arch. venez. pueric. pediatr
Journal subject:
Pediatrics
Year:
2008
Type:
Article
Affiliation country:
Venezuela
Institution/Affiliation country:
Hospital de Niños J.M de Los Ríos/VE
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