Carcinoma adenoide cístico intracraniano / Intracranial adenoid cystic carcinoma

RESUMO

Os carcinomas adenoides císticos são tumores de crescimento lento, localmente agressivos e com tendência à recorrência. Têm particular interesse por infiltrar estruturas neurais e disseminar-se pelo perineuro. Envolvimento intracraniano é raro. Descreve-se um caso de carcinoma adenoide cístico originado na glândula lacrimal esquerda e invasão do seio cavernoso. Ressonância magnética demonstrou lesão tumoral, extra-axial, bem delimitada, semelhante a um meningioma da asa do esfenoide com invasão do seio cavernoso. O paciente apresentou boa resposta ao tratamento com cirurgia e radioterapia complementar.

ABSTRACT

Adenoid cystic carcinoma is a relatively common head and neck tumor that is slow growing, but locally aggressive and thus prone to recurrence. It is of particular interest because of its tendency to locally infiltrate neural structures and to spread perineurally. Intracranial involvement has been regarded as rare. A case report of a patient with adenoid cystic carcinoma originated in the left lacrimal gland and involving the cavernous sinus is presented. Magnetic resonance image demonstrated a welldemarcated enhancing extra-axial tumour, resembling a sphenoid ridge meningioma extending into the cavernous sinus. This patient showed a good response to treatment with surgery followed by post-operative radiotherapy.