Encefalocele basal esfenoetmoidal associada a fissura labiopalatina mediana: relato de caso / Basal sphenoethmoidal encephalocele in association with midline cleft lip and palate: case report
Radiol. bras
;
44(6): 399-400, nov.-dez. 2011. ilus
Article
in Portuguese
| LILACS
| ID: lil-611522
RESUMO
Associação de encefalocele basal esfenoetmoidal com fissura labiopalatina é extremamente rara. Relatamos um caso de uma criança de nove anos de idade apresentando uma fissura facial mediana com meningocele, que era evidente através da falha do palato como uma massa mediana intranasal pulsátil. Uma análise dos aspectos clínicos e radiológicos deste caso de disrafia craniana foi realizada.
ABSTRACT
Association of basal sphenoethmoidal encephalocele with midline cleft lip and palate is extremely rare. The authors report the case of a nine-year-old girl presenting a midline facial cleft with meningocele that was noticeable through the palatine defect as a medial intranasal pulsatile mass. An analysis of clinical and radiological findings of the present case of cranial dysraphism is carried out.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Skull
/
Congenital Abnormalities
/
Cleft Palate
/
Rare Diseases
/
Encephalocele
/
Meningocele
Type of study:
Risk factors
Limits:
Child
/
Female
/
Humans
Language:
Portuguese
Journal:
Radiol. bras
Journal subject:
Diagnostic Imaging
/
Radiology
Year:
2011
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Universidade Federal da Paraíba/BR
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