Síndrome de Shone incompleto: a propósito de un caso diagnosticado en la adultez / Incomplete Shone's syndrome. Apropos of a case diagnosed in adulthood
Rev. cuba. med
;
51(3): 267-271, jul.-set. 2012.
Article
in Spanish
| LILACS
| ID: lil-649864
RESUMEN
El síndrome de Shone constituye una rara entidad cardíaca congénita que consiste en la presencia de lesiones estructurales obliterantes de hemicardio izquierdo que incluyen anillo supravalvular, válvula mitral en paracaídas, estenosis sub-aórtica y coartación aórtica. Es poco frecuente que curse en su forma incompleta. El caso que a continuación se presenta, describe el síndrome de Shone incompleto detectado en un adulto
ABSTRACT
Shone's syndrome is a rare congenital heart disease consisting in the presence of obliterating structural lesions on the left side of the heart, including supravalvular ring, parachute mitral valve, subaortic stenosis and aortic coarctation. The incomplete form of the disease is not common. The presentation describes a case of incomplete Shone's syndrome diagnosed in adulthood
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Cardiovascular Diseases
Type of study:
Diagnostic study
Limits:
Adult
/
Humans
/
Male
Language:
Spanish
Journal:
Rev. cuba. med
Journal subject:
Medicine
Year:
2012
Type:
Article
Affiliation country:
Cuba
Institution/Affiliation country:
Hospital Clinicoquirúrgico Hermanos Ameijeiras/CU
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