Linfoma tipo hidroa: presentación de un caso / Hydroa-like lymphoma: a case report
Dermatol. peru
;
21(3): 126-129, jul.-sept. 2011. ilus
Article
in Spanish
| LILACS, LIPECS
| ID: lil-671772
RESUMEN
El linfoma tipo hidroa es un linfoma cutáneo primario T/NK raro, que viene siendo reportado en países de Asia y Latinoamérica, en la que se ha hallado asociación con infección crónica activa por virus de Epstein-Barr. Se presenta el caso de una paciente de 14 años con un tiempo de enfermedad de tres años, en el que inicialmente presenta eritema y vesiculación de áreas fotoexpuestas de manera episódica y que posteriormente presenta edema facial marcado con zonas violáceas, disminución de peso y falla multiorganica a la que se le hace diagnóstico post mórtem de linfoma tipo hidroa.
ABSTRACT
Hydroa like-lymphoma is a rare T/NK primary cutaneous lymphoma, which has been reported in people from Asia and Latin-America and has been associated to Epstein-Barr virus (EBV) chronic latent infection. We present the case of a 14 year-old patient with a time since diagnosis of illness of three years. She initially has erythema and vesiculation in sun-exposed areas that appears in a episodic way and then adds overt facial edema and purpuric patches, wasting, weight loss and multiorganic failure. The diagnosis of hydroa-like lymphoma was done post-mortem.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Lymphoma, T-Cell, Cutaneous
/
Hydroa Vacciniforme
/
Medical Illustration
/
Multiple Organ Failure
Limits:
Adolescent
/
Female
/
Humans
Language:
Spanish
Journal:
Dermatol. peru
Year:
2011
Type:
Article
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