Keratocystic odontogenic tumor related to nevoid basal cell carcinoma syndrome: clinicopathological study
Braz. j. oral sci
;
12(1): 23-29, jan.-mar. 2013. ilus, tab
Article
in English
| LILACS, BBO
| ID: lil-671928
ABSTRACT
Aim:
To assess clinicopathological features of patients with keratocystic odontogenic tumor (KCOT) associated with nevoid basal cell carcinoma syndrome (NBCCS) in a single Brazilian institution.Methods:
After histopathological analyses of KCOT related to NBCCS, the medical charts of 14 patients were assessed. These patients presented a total of 31 primary and 8 recurrent KCOT.Results:
Out of 14 patients, 8 presented a single KCOT, 4 showed synchronous tumors, 1 had3 metachronous lesions and another patient had 2 synchronous lesions at initial evaluation and then developed other 3 metachronous lesions. Besides the 31 primary KCOTs, 18 lesions were located in mandible and 13 in maxilla. Most tumors presented unilocular pattern and association with a tooth.Conclusions:
KCOT is a frequent manifestation of NBCCS and can be its first sign, mainly in young patients. In contrast to a previously published series, most patients presented a single lesion.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Carcinoma
/
Basal Cell Nevus Syndrome
Limits:
Female
/
Humans
/
Male
Language:
English
Journal:
Braz. j. oral sci
Journal subject:
Dentistry
Year:
2013
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Universidade de São Paulo/BR
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