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Pyoderma gangrenosum with renal and splenic impairment - case report / Manifestacao esplenica e renal do pioderma gangrenoso - relato de caso
Carvalho, Luciana Rabelo de; Zanuncio, Virginia Vinha; Gontijo, Bernardo.
  • Carvalho, Luciana Rabelo de; Federal University of Minas Gerais. Teaching Hospital. Dermatology Unit. Belo Horizonte. BR
  • Zanuncio, Virginia Vinha; Federal University of Minas Gerais. Teaching Hospital. Dermatology Unit. Belo Horizonte. BR
  • Gontijo, Bernardo; Federal University of Minas Gerais. Teaching Hospital. Dermatology Unit. Belo Horizonte. BR
An. bras. dermatol ; 88(6,supl.1): 150-153, Nov-Dec/2013. graf
Article in English | LILACS | ID: lil-696783
ABSTRACT
Pyoderma gangrenosum is an uncommon and recurrent neutrophilic dermatosis of unknown cause. The lesions usually start as tender sterile papulopustules or erythematous nodules that undergo necrosis followed by ulceration. The lower limbs are most commonly affected and around half of the cases are associated with systemic disorders. Although rare, cases of pyoderma gangrenosum with extramucocutaneous sterile neutrophilic infiltrate have been reported, with the lungs being the most commonly affected organ. We report a case of pyoderma gangrenosum with splenic and renal impairment. Pyoderma gangrenosum should be considered a multisystemic disease with classic cutaneous manifestations and potential involvement of internal organs.
RESUMO
Pioderma gangrenoso é uma dermatose neutrofílica incomum, recorrente e de etiologia desconhecida. As lesões geralmente se iniciam como papulopústulas estéreis ou nódulos eritematosos que sofrem necrose seguida de ulceração. Os membros inferiores são mais comumente afetados e quase a metade dos casos está associada a doenças sistêmicas. Apesar de raros, casos de pioderma gangrenoso com infiltrado neutrofílico estéril extramucocutâneo foram relatados e os pulmões são os órgãos mais comumente acometidos. Nós relatamos um caso de manifestação esplênica e renal do pioderma gangrenoso. Pioderma gangrenoso deve ser considerado doença multissistêmica com manifestações cutâneas clássicas e potencial envolvimento de órgãos internos.
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Full text: Available Index: LILACS (Americas) Main subject: Splenic Diseases / Pyoderma Gangrenosum / Kidney Diseases Limits: Female / Humans Language: English Journal: An. bras. dermatol Journal subject: Dermatology Year: 2013 Type: Article Affiliation country: Brazil Institution/Affiliation country: Federal University of Minas Gerais/BR

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Full text: Available Index: LILACS (Americas) Main subject: Splenic Diseases / Pyoderma Gangrenosum / Kidney Diseases Limits: Female / Humans Language: English Journal: An. bras. dermatol Journal subject: Dermatology Year: 2013 Type: Article Affiliation country: Brazil Institution/Affiliation country: Federal University of Minas Gerais/BR