Do you know this syndrome? / Voce conhece esta sindrome?
An. bras. dermatol
;
88(6): 1009-1010, Nov-Dec/2013. graf
Article
in English
| LILACS
| ID: lil-699012
ABSTRACT
POEMS syndrome is a unique clinical entity, the diagnosis of which is made when polyneuropathy and monoclonal gammopathy occur together, associated with other changes such as organomegaly, endocrinopathy, skin changes and papilledema. Cutaneous manifestations are heterogeneous, with diffuse cutaneous hyperpigmentation, hemangiomas and hypertrichosis occurring more frequently. We report the case of a 65- year-old female patient with this syndrome, diagnosed after 15 years of disabling peripheral neuropathy.
RESUMO
A síndrome de POEMS é uma entidade clínica única cujo diagnóstico é colocado quando existe polineuropatia e gamapatia monoclonal associada a outras alterações tais como organomegalia, endocrinopatia, alterações cutâneas e papiledema. As manifestações cutâneas são heterogéneas, sendo as mais frequentes a hiperpigmentação cutânea difusa, os hemangiomas e a hipertricose. Relata-se o caso de uma doente de 65 anos com essa síndrome diagnosticada após 15 anos de neuropatia periférica.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Hypotrichosis
/
Macular Degeneration
Type of study:
Diagnostic study
Limits:
Adolescent
/
Female
/
Humans
Language:
English
Journal:
An. bras. dermatol
Journal subject:
Dermatology
Year:
2013
Type:
Article
Affiliation country:
Portugal
Institution/Affiliation country:
Centro Hospitalar de Lisboa Central/PT
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