Incontinentia pigmenti
An. bras. dermatol
;
89(1): 26-36, Jan-Feb/2014. tab, graf
Article
in English
| LILACS
| ID: lil-703556
ABSTRACT
Incontinentia pigmenti is a rare genodermatosis in which the skin involvement occurs in all patients. Additionally, other ectodermal tissues may be affected, such as the central nervous system, eyes, hair, nails and teeth. The disease has a X-linked dominant inheritance pattern and is usually lethal to male fetuses. The dermatological findings occur in four successive phases, following the lines of Blaschko First phase - vesicles on an erythematous base; second phase - verrucous hyperkeratotic lesions; third phase - hyperchromic spots and fourth phase - hypochromic atrophic lesions.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Skin
/
Incontinentia Pigmenti
Type of study:
Etiology study
Limits:
Humans
/
Male
Language:
English
Journal:
An. bras. dermatol
Journal subject:
Dermatology
Year:
2014
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Porto Alegre Health Sciences Federal University/BR
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