Clouston syndrome associated with eccrine syringofibroadenoma
An. bras. dermatol
;
89(3): 504-506, May-Jun/2014. graf
Article
in English
| LILACS
| ID: lil-711619
ABSTRACT
Eccrine syringofibroadenoma is a rare benign neoplasia derived from acrosyryngium cells of the eccrine sudoriferous glands. It affects the extremities of elderly individuals as solitary tumors, or may also present as multiple lesions. There are controversies about the pathogenesis and differentiation of the tumor. Eccrine syringofibroadenoma has been associated with subjacent conditions, such as for example, hypohidrotic ectodermic dysplasias. The authors describe a case report of a patient with Clouston Syndrome, who presented papules and nodules in extremities, clinically and histologically compatible with eccrine syringofibroadenoma. There are only three cases described in the literature, associated with Clouston Syndrome, and this is the fourth case.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Sweat Gland Neoplasms
/
Ectodermal Dysplasia
/
Fibroadenoma
/
Eccrine Glands
Type of study:
Risk factors
Limits:
Adult
/
Female
/
Humans
Language:
English
Journal:
An. bras. dermatol
Journal subject:
Dermatology
Year:
2014
Type:
Article
Affiliation country:
Brazil
Institution/Affiliation country:
Universidade Estadual do Sudoeste da Bahia/BR
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