Incontinencia pigmenti: a propósito de dos casos / Incontinentia pigmenti: report of two cases
Rev. chil. dermatol
;
28(2): 160-166, 2012. ilus
Article
in Spanish
| LILACS
| ID: lil-718976
RESUMEN
La Incontinencia Pigmenti (IP) o síndrome de Bloch Sulzberger es un trastorno multisistémico neuroectodérmico, que afecta predominantemente al género femenino, cuya manifestación inicial incluye lesiones cutáneas que evolucionan por brotes. En ocasiones, se asocia a compromiso oftalmológico, neurológico y dentales parte del diagnóstico diferencial de lesiones ampollares en un neonato. Se presentan dos casos de IP diagnosticados en etapas cutáneas distintas, uno de ellos con compromiso neurológico.
ABSTRACT
Incontinentia Pigmenti (IP) or Bloch Sulzberger syndrome is a neuroectodermal multisystemic disorder, that predominantly affects women, whose initial manifestation includes skin lesions that evolve by outbreaks. Sometimes, is associated with ophthalmological, neurological and dental commitment. It is part of the differential diagnosis of bullous lesions in a newborn. We present 2 cases of IP diagnosed in different skin stages and one of them with neurological involvement.
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Index:
LILACS (Americas)
Main subject:
Incontinentia Pigmenti
Type of study:
Diagnostic study
/
Etiology study
Limits:
Female
/
Humans
/
Infant, Newborn
Language:
Spanish
Journal:
Rev. chil. dermatol
Journal subject:
Dermatology
Year:
2012
Type:
Article
Affiliation country:
Chile
Institution/Affiliation country:
CESFAM Santa Fe/CL
/
Hospital Las Higueras de Talcahuano/CL
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