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The case of a boy with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita: a unique instance of phacomatosis pigmentovascularis
MA, Han; Liao, Mengsi; Qiu, Shu; Luo, Ruijun; Lu, Rongbiao; Lu, Chun.
Affiliation
  • MA, Han; Sun Yat-sen Universit. Third Affi liated Hospital. CN
  • Liao, Mengsi; Sun Yat-sen Universit. Third Affi liated Hospital. CN
  • Qiu, Shu; Sun Yat-sen Universit. Third Affi liated Hospital. CN
  • Luo, Ruijun; Sun Yat-sen Universit. Third Affi liated Hospital. CN
  • Lu, Rongbiao; Sun Yat-sen Universit. Third Affi liated Hospital. CN
  • Lu, Chun; Sun Yat-sen Universit. Third Affi liated Hospital. CN
An. bras. dermatol ; 90(3,supl.1): 10-12, May-June 2015. tab, ilus
Article in En | LILACS | ID: lil-755755
Responsible library: BR1.1
ABSTRACT
Abstract

Phacomatosis pigmentovascularis is a rare, congenital condition characterized by a combination of cutaneous melanocytic lesions and vascular malformation. We discuss an entirely unique case of Phacomatosis pigmentovascularis with nevus of Ota, extensive Mongolian spot, nevus flammeus, nevus anemicus and cutis marmorata telangiectatica congenita, which may represent a heretofore undescribed variant of phacomatosis pigmentovascularis.

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Full text: 1 Index: LILACS Main subject: Skin Neoplasms / Telangiectasis / Nevus of Ota / Skin Diseases, Vascular / Port-Wine Stain / Neurocutaneous Syndromes / Mongolian Spot Limits: Humans / Male Language: En Journal: An. bras. dermatol Journal subject: DERMATOLOGIA Year: 2015 Type: Article

Full text: 1 Index: LILACS Main subject: Skin Neoplasms / Telangiectasis / Nevus of Ota / Skin Diseases, Vascular / Port-Wine Stain / Neurocutaneous Syndromes / Mongolian Spot Limits: Humans / Male Language: En Journal: An. bras. dermatol Journal subject: DERMATOLOGIA Year: 2015 Type: Article