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Clouston Syndrome: 25-year follow-up of a patient
Trídico, Lívia Arroyo; Antonio, João Roberto; Pozetti, Eurides Maria de Oliveira; Rosa, Ana Maria Mendes; Antonio, Carlos Roberto.
  • Trídico, Lívia Arroyo; Faculdade de Medicina de São José do Rio Preto. São José do Rio Preto. BR
  • Antonio, João Roberto; Faculdade de Medicina de São José do Rio Preto. São José do Rio Preto. BR
  • Pozetti, Eurides Maria de Oliveira; Faculdade de Medicina de São José do Rio Preto. São José do Rio Preto. BR
  • Rosa, Ana Maria Mendes; Faculdade de Medicina de São José do Rio Preto. São José do Rio Preto. BR
  • Antonio, Carlos Roberto; Faculdade de Medicina de São José do Rio Preto. São José do Rio Preto. BR
An. bras. dermatol ; 90(6): 897-899, Nov.-Dec. 2015. graf
Article in English | LILACS | ID: lil-769510
ABSTRACT
Abstract Clouston syndrome is a rare genodermatosis that affects skin and annexes. It is a form of ectodermal dysplasia characterized by generalized hypotrichosis, palmoplantar hyperkeratosis and nail dystrophy. This paper reports a 25-year follow-up of a patient with Clouston syndrome, from childhood to adulthood, monitoring diagnosis and clinical course of the disease.
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Full text: Available Index: LILACS (Americas) Main subject: Ectodermal Dysplasia Type of study: Observational study / Prognostic study Limits: Adult / Female / Humans Language: English Journal: An. bras. dermatol Journal subject: Dermatology Year: 2015 Type: Article Affiliation country: Brazil Institution/Affiliation country: Faculdade de Medicina de São José do Rio Preto/BR

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Full text: Available Index: LILACS (Americas) Main subject: Ectodermal Dysplasia Type of study: Observational study / Prognostic study Limits: Adult / Female / Humans Language: English Journal: An. bras. dermatol Journal subject: Dermatology Year: 2015 Type: Article Affiliation country: Brazil Institution/Affiliation country: Faculdade de Medicina de São José do Rio Preto/BR