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Síndrome de Wolff-Parkinson-White com Hipertrofia Ventricular: Preditores de Eventos / Wolff-Parkinson-White Syndrome and Ventricular Hypertrophy: Events Predictors
van der Steld, Lenises de Paula; Rocha, Mario de Seixas.
  • van der Steld, Lenises de Paula; Escola Bahiana de Medicina e Saúde Pública. Salvador. BR
  • Rocha, Mario de Seixas; Escola Bahiana de Medicina e Saúde Pública. Salvador. BR
Int. j. cardiovasc. sci. (Impr.) ; 28(3): 224-233, mai.-jun. 2015. tab, ilus, graf
Article in Portuguese | LILACS | ID: lil-775245
RESUMO
Fundamentos A síndrome do PRKAG2 é classificada como uma doença de armazenamento de glicogênio, caracterizada pela presença da síndrome de Wolff-Parkinson-White (WPW), hipertrofia ventricular (HV) e doençado sistema de condução (DSC).

Objetivos:

Identificar potenciais fatores prognósticos para eventos em indivíduos acometidos por essa doença edescrever as características clínicas.

Métodos:

Sessenta indivíduos foram acompanhados de março de 2005 a março de 2015, estratificados em doisgrupos Grupo 1 (G1) - portadores de WPW, HV ou ambos; e Grupo 2 (G2) - indivíduos assintomáticos, comexame físico, eletrocardiograma e ecocardiograma normais. Realizados anamense, exame físico, eletrocardiograma e ecocardiograma. Quando necessário, realizou-se Holter e estudo eletrofisiológico.

Resultados:

Dos 60 indivíduos selecionados, 18 constituíram o G1. Destes, 11 (61,1%) tinham HV associada à WPW, 6 (33,3%) apresentavam WPW isolada e 1 (5,6%) paciente apresentava HV isolada. A média de idade foi 27,0±16,0 anos e 32 (53,3%) eram do sexo masculino. Apenas indivíduos do Grupo 1 apresentaram eventos isolados 3 (17,0%) paradas cardíacas, 2 (11,0%) mortes súbitas, 6 (33,0%) implantes de marca-passo, 4 (22,0%) acidentes isquêmicos encefálicos transitórios e 9 (50,0%) eventos combinados. Os potenciais preditores de eventos combinados foram tamanho de átrio esquerdo (p=0,07) diabetes mellitus (p=0,05) e os bloqueios atrioventriculares (p=0,019). Esses fatores não evidenciaram significância estatística, quando comparados na análise de regressão de Cox.

Conclusões:

Em portadores de WPW com hipertrofia ventricular ocorreu associação entre diabetes mellitus, bloqueio atrioventricular e tamanho de átrio esquerdo com os principais desfechos.
ABSTRACT

Background:

The PRKAG2 syndrome is classified as a glycogen storage disease, characterized by the presence of the Wolff Parkinson-Whitesyndrome (WPW), ventricular hypertrophy (VH) and conduction system disease (CSD).

Objectives:

Finding potential prognostic factors for events in individuals affected by this disease and describing the clinical characteristics.

Methods:

Sixty individuals were monitored from March 2005 to March 2015, being divided into two groups Group 1 (G1) - patients with WPW, VH or both; and Group 2 (G2) - asymptomatic patients, with normal physical examination, electrocardiogram and echocardiography. It included the performance of medical history, physical examination, electrocardiogram and echocardiogram. Holter and electrophysiological study were performed when necessary.

Results:

G1 was made of 18 out of the 60 patients selected. Of these, 11 (61.1%) had VH related to WPW, 6 (33.3%) had isolated WPW and 1 (5.6%) patient had isolated VH. The mean age was 27.0±16.0 years and 32 (53.3%) were male. Only the patients in Group 1 had isolated events 3 (17.0%) cardiac arrests, 2 (11.0%) sudden deaths, 6 (33.0%) pacemaker implants, 4 (22.0%) transient ischemic attacks and 9 (50.0%) combined events. The events predictors in potential combined were left atrium size (p=0.07) diabetes mellitus (p=0.05) and the atrioventricular blocks (p=0.019). Those factors did not have statistic significance when compared in the Cox regression analysis.

Conclusions:

In WPV patients with ventricular hypertrophy there was an association of diabetes mellitus, atrioventricular blockand left atrium size with the main outcomes.
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Index: LILACS (Americas) Main subject: Wolff-Parkinson-White Syndrome / Risk Factors / Death, Sudden, Cardiac / Hypertrophy, Left Ventricular Type of study: Diagnostic study / Etiology study / Incidence study / Observational study / Prognostic study / Risk factors Limits: Adult / Female / Humans / Male Language: Portuguese Journal: Int. j. cardiovasc. sci. (Impr.) Journal subject: Cardiology Year: 2015 Type: Article Affiliation country: Brazil Institution/Affiliation country: Escola Bahiana de Medicina e Saúde Pública/BR

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Index: LILACS (Americas) Main subject: Wolff-Parkinson-White Syndrome / Risk Factors / Death, Sudden, Cardiac / Hypertrophy, Left Ventricular Type of study: Diagnostic study / Etiology study / Incidence study / Observational study / Prognostic study / Risk factors Limits: Adult / Female / Humans / Male Language: Portuguese Journal: Int. j. cardiovasc. sci. (Impr.) Journal subject: Cardiology Year: 2015 Type: Article Affiliation country: Brazil Institution/Affiliation country: Escola Bahiana de Medicina e Saúde Pública/BR