Epidermodisplasia verruciforme: reporte de una serie de casos / Epidermodysplasia verruciformis: report of a case series
Folia dermatol. peru
;
23(2): 67-72, may.-ago.2012. ilus, tab
Article
in Spanish
| LILACS, LIPECS
| ID: lil-786451
RESUMEN
La epidermodisplasia verruciforme es una genodermatosis rara que condiciona una susceptibilidad anormal a infecciones por el virus del papiloma humano, presentando lesiones cutáneas con potencial oncogénico. Objetivo:
determinar la frecuencia de epidermodisplasia verruciforme y caracterizas los hallazgos demográficos, clínicos y terapéuticos de los pacientes que acudieron a la Cátedra de Dermatología del Hospital de Clínicas, entre los años 2003, 2012. Material ymétodos:
se realizó un estudio descriptico de pacientes con diagnóstico clínico e histopatológico de epidermodisplasia verruciforme.Resultados:
se encontraron cinco casos. Todos los pacientes iniciaron el cuadro en la infancia y presentaron lesiones tipo pitiriasis versicolor y verrugas planas. Todos refirieron exposición solar crónica y familiares de primer grado con la misma enfermedad. La neoplasia más frecuente fue al enfermedad de Bowen, seguida del carcinoma epidermoide infiltrante. Los tratamientos incluyeron cirugía, crioterapia y 5-fluorouracilo tópico...ABSTRACT
Epidermodysplasia verruciformis is a rare genodermatosis characterized by an abnormal susceptibility to human papiloma virus infection, developing cutaneous lesions with oncogenic potential. Objective:
To determine the frequency, clinical demographic and therapeutic characteristics of patients who attend to the Dermatology Department of the Hospital de Clinicas between 2003 and 2012.Methods:
A descriptive study of patients with clinical and histopathological diagnosis of epidermodysplasia verruciformis was carried out.Results:
Five cases were found. Childhood-onset of disease, pityriasis versicolor-like lesions and flat warts were seen in all cases. All patients reported chronic sun exposure and first-degree relatives with the same disease. BowenÆs disease was the most frequent neoplasm, followed by invasive squamous cell carcinoma. Treatment modalities included surgery, cryotherapy and topical 5 fluorouracil.Discussion:
Consistently to the infrequent nature of the disease, only five cases were diagnosed in the years. Unlike other studies, BowenÆs disease was the predominant neoplasm...
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Skin Neoplasms
/
Epidermodysplasia Verruciformis
/
Bowen's Disease
/
Papillomavirus Infections
Limits:
Humans
Language:
Spanish
Journal:
Folia dermatol. peru
Year:
2012
Type:
Article
Institution/Affiliation country:
Universidad Nacional de Asunción/PY
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