Compromiso renal en síndrome de Poems: caso clínico / Chronic kidney disease associated with Poems syndrome: report of one case
Rev. méd. Chile
;
144(4): 516-520, abr. 2016. ilus
Article
in Spanish
| LILACS
| ID: lil-787124
ABSTRACT
POEMS syndrome is characterized by Polyneuropathy, Organomegaly, Endocrinopathy, Monoclonal protein and Skin changes. We report a woman with the syndrome, who had peripheral polyneuropathy, osteosclerotic myeloma, monoclonal IgA elevation, hypothyroidism, hypogonadotrophic hypogonadism, hyperprolactinemia, adrenal insufficiency, hepatosplenomegaly, lymphadenopathy, thyroid and parotid enlargement, Castlemans disease, papilledema, stiff and hyperpigmented skin, white nails, clubbing, ascites and chronic diarrhea. She had also a nephropathy characterized by microscopic hematuria, proteinuria, renal insufficiency and a unilateral kidney retraction. She was treated with melphalan and prednisone, achieving remission of the disease and nephropathy. She survived twelve years and died due to a myocardial infarction 20 years after POEMS diagnosis.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
POEMS Syndrome
/
Renal Insufficiency, Chronic
Type of study:
Risk factors
Limits:
Adult
/
Female
/
Humans
Language:
Spanish
Journal:
Rev. méd. Chile
Journal subject:
Medicine
Year:
2016
Type:
Article
Affiliation country:
Chile
Institution/Affiliation country:
Universidad de Valparaíso/CL
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