Anemia de células falciformes / Sickle-cell anemia
Repert. med. cir
;
23(3): 221-225, 2014.
Article
in English, Spanish
| LILACS, COLNAL
| ID: lil-795679
RESUMEN
Presentamos dos mujeres que consultaron a urgencias por dolor abdominal agudo, iniciado pocas horas después de su llegada a Bogotá DC, asociado con síndrome anémico y hallazgos paraclínicos sugestivos de anemia de células falciformes, que se confirmó con electroforesis de proteínas en la consulta externa. La drepanocitosis, conocida como anemia de células falciformes, es una hemoglobinopatía estructural de causa genética que ocasiona clínica vasoclusiva con isquemia tisular secundaria generadora de crisis de dolor, que se exacerba entre otras razones por cambios de temperatura y de la presión del oxígeno atmosférico. Es importante causa de dolor agudo en pacientes de raza negra que asisten a urgencias al provenir con frecuencia de lugares cálidos.
ABSTRACT
We report the cases of two women who consulted to the emergency department due to abdominal pain that started afew hours after arriving to Bogotá DC, associated with anemic syndrome and laboratory tests findings suggestive ofsickle-cell anemia confirmed by protein electrophoresis in the outpatient clinic. Drepanocytosis, or sickle-cell anemia,is an inherited structural hemoglobin disorder manifested by vaso-occlusive crises followed by secondary is chemictissue injury generating pain crises, which exacerbate, among other reasons, due to changes in temperature and ofatmospheric oxygen pressure. It is an important cause of acute pain in the black population who visit the emergency room when arriving most commonly from places at low altitude.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Hemoglobinopathies
/
Anemia, Sickle Cell
Limits:
Adult
/
Female
/
Humans
Language:
English
/
Spanish
Journal:
Repert. med. cir
Journal subject:
Cirurgia Geral
/
Medicina
Year:
2014
Type:
Article
Affiliation country:
Colombia
Institution/Affiliation country:
Fundación Universitaria de Ciencias de la Salud/CO
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