Esclerose tuberosa com rabdomioma de ventrículo esquerdo / Tuberous sclerosis associated with a left ventricle rabdomioma
Arq. bras. cardiol
;
55(6): 381-383, dez. 1990. ilus
Article
in Portuguese
| LILACS
| ID: lil-91438
RESUMO
Lactente do sexo feminino com espasmos em flexäo, manchas hipocrômicas na pele e sopro sistólico de ejeçäo. O diagnóstico clínico, apoiado por tomografia de crânio e neurossonografia, foi de esclerose tuberosa. Ecocardiograma e cineangiocardiografia revelaram tumor em via de saída do ventrículo esquerdo associado. Após a ressecçäo do rabdomioma a paciente evoluiu assintomática, controlado o quadro neurológico com ácido valpróico
ABSTRACT
Female infant, presenting with flexion spasms, skin hypochromatic spots and systolic ejection murmur. A clinical diagnosis of tuberous sclerosis, supported by computerized brain tomography and neurossonographic data, was made. Echocardiographic and cineangiocardiographic studies disclosed an associated tumor in left ventricle outlet. After ressection of the rhabdomyoma, the patient is assymptomatic with neural manifestations controlled under valproic acid.
Full text:
Available
Index:
LILACS (Americas)
Main subject:
Rhabdomyoma
/
Tuberous Sclerosis
/
Heart Neoplasms
Type of study:
Diagnostic study
/
Risk factors
Limits:
Female
/
Humans
/
Infant
Language:
Portuguese
Journal:
Arq. bras. cardiol
Journal subject:
Cardiology
Year:
1990
Type:
Article
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