Extrahepatic portal hypertension due to familial protein S deficiency.
Indian Pediatr
;
2009 Jan; 46(1): 70-1
Article
in English
| IMSEAR
| ID: sea-12211
ABSTRACT
Portal vein thrombosis (PVT) is a common cause of portal hypertension in children. A majority of children with PVT of unknown etiology have functional Protein C deficiency or abnormally elevated levels of anti-cardiolipin antibodies. We report an 8 years old Indian girl with portal cavernoma due to hereditary Protein S deficiency. We documented familial deficiency of Protein S in 2 asymptomatic siblings suggesting that this deficiency is the primary cause of portal vein thrombosis.
Full text:
Available
Index:
IMSEAR (South-East Asia)
Main subject:
Portal Vein
/
Female
/
Humans
/
Child
/
Protein S Deficiency
/
Venous Thrombosis
/
Hypertension, Portal
Language:
English
Journal:
Indian Pediatr
Year:
2009
Type:
Article
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