Spontaneous lens dislocation.

ABSTRACT

We present a multidisciplinary approach to a patient with spontaneous lens dislocation. A 39-year-old female developed blurred vision in both eyes one year prior to presentation. This symptom could not be corrected with spectacles. Her previous history showed progressive bilateral myopia since the age of ten and a single episode of syncope without exertion 16 months before presentation. Ophthalmic examination demonstrated cataracts with upward and outward displacement of the crystalline lenses in both eyes. Manifest refraction and keratometry displayed moderate myopia with high lenticular astigmatism in both eyes. Marfan syndrome was suspected on the basis of general physical examination and a complete cardiovascular examination performed by the geneticist and the cardiologist respectively. In addition, the role of the cardiovascular-thoracic surgeon in the management of Marfan syndrome is presented.